Fibrous dysplasia and aneurysmal bone cyst of the skull base presenting with blindness: a report of a rare locally aggressive example

Terkawi, Abdullah Sulieman; Al-Qahtani, Khalid H; Baksh, Eman; Soualmi, Lahbib; Mohamed, Asim El-Bagir; Sabbagh, Abdulrahman J

doi:10.1186/1758-3284-3-15

Table 1 Clinical, radiological findings, and treatment of reported combined fibrous dysplasia and aneurysmal bone cyst of the skull

From: Fibrous dysplasia and aneurysmal bone cyst of the skull base presenting with blindness: a report of a rare locally aggressive example

Reference	Age (years) Gender	Site	Clinical presentation	Radiological findings	Treatment/Surgical approach	Follow-up
Składzień et al., 2008 [8]	16/M	Rt Maxillary, orbital	Epistaxis and chronic rhinosinusitis	Large cystic lesion	En-bloc excision	9 mo disease free
Rappaport, 1989 [9]	25/M	Lt occipital	Painful mass	CT: pagetoid changes and hypodense lesion	Surgical excision	No f/u
Wojno and McCathy, 1994 [10]	14/F	Rt temporal	Painless mass	CT: nonhomogeneous cystic lesion	Surgical excision	2 yr disease free
Wojno and McCathy, 1994 [10]	40/M	Lt frontal	Expanding mass Mass appear after head trauma	CT: diffuse thickening of the calvarium, Lt frontal cyst	Surgical excision	No f/u
Haddad et al., 1998 [11]	6.5/M	Rt temporal	Rt painless temporal mass	CT: nonhomogeneous cystic mass.	Frontotemporal excision	4 yr disease free
Saito et al. 1998 [12]	11/M	nasal cavity, sphenoid bone, and skull base	Nasal obstruction and headache for 1 yr	CT and MRI, irregular multilobulated tumor	Craniofacial excision	3.5 yr disease free
Branch et al., 1986 [13]	9/F	Lt parietal & fronto-temporal	Painful Lt and frontal parietal mass for 1 mo	CT: large cystic bone lesion in the parietal area	Surgical excision	No f/u
Branch et al., 1986 [13]	19/M	Rt parietal	Painless mass k/c of FD for 15 yr	CT: cystic expansion of the skull	Surgical excision	No f/u
Itshayek et al., 2002 [14]	19/M	Lt occipital bone and clivus	Painless mass of the occipital area	CT: occipital cyst lesion	Selective embolization. Followed by surgical resection.	1 yr disease free
Pasquini et al., 2002 [15]	5/M	Rt maxillary sinus	Progressive and persistent Rt side epiphora and rhinosinusitis for 2 yr.	CT: Cyst-like lesion.	Transnasal endoscopic surgery	No f/u
Lin et al., 2004 [16]	18/M	Lt frontal bone	Progressive enlargement of the mass with severe headache	CT: several expansile cystic spaces	Surgical resection	No f/u
Iseri et al., 2005 [17]	35/F	Lt occipital bone	Progressive severe headache	FD of clivus, temporal, and occipital bones.	Unresectable
Mattei et al., 2005 [18]	19/M	Occipital bone	As SAH; severe headache and nuchal rigidity.	Hemmorage and cyst	Partial surgical resection	No f/u
Our case	7/F	Sphenoidal and ethmoidal bones	Lt eye loss of vision Lt nasal obstruction	Cystic expansible lesion	Endonasal - cranial resection	Recur after 5 mo

FD; fibrous dysplasia. AG; angiogram. LPMA; Lt posterior meningeal artery. SAH; subarachnoid hemorrhage. ABC; aneurysmal bone cyst. f/u; follow up. k/c; known case.
PNS; paranasal sinuses.

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Head & Neck Oncology